What is fibromatosis desmoid?

What is fibromatosis desmoid?

Desmoid fibromatosis (DF) is a locally aggressive, deep seated connective tissue malignancy developing in musculoaponeurotic tissues. It is also known as aggressive fibromatosis, deep fibromatosis, musculoaponeurotic fibromatosis and desmoid tumor.

Is fibromatosis a desmoid tumor?

Desmoid tumors are also known as aggressive fibromatosis or desmoid-type fibromatosis. A desmoid tumor can occur anywhere in the body since connective tissue is found everywhere in your body. Desmoid tumors are often found in the abdomen, as well as the shoulders, upper arms, and thighs.

How is desmoid fibromatosis treated?

Treatments for desmoid tumors include:

1. Monitoring the growth of the tumor. If your desmoid tumor causes no signs or symptoms, your doctor may recommend monitoring the tumor to see if it grows.
2. Surgery.
3. Radiation therapy.
4. Chemotherapy and other medications.

What are the symptoms of desmoid tumors?

Desmoid Tumor: Symptoms and Signs

• Soreness or pain caused by the tumor pressing on nearby nerves, muscles, or blood vessels.
• Tingling or a feeling of “pins and needles,” when the tumor presses on local nerves or blood vessels.
• Limping or other difficulties moving the legs or feet.
• Difficulty moving the arms or hands.
• Pain.

How common is desmoid fibromatosis?

Desmoid tumors are rare, making up less than 3% of all soft-tissue tumors. Each year, approximately 900 to 1,500 people in the United States will be diagnosed with a desmoid tumor.

Can a desmoid tumor be fatal?

Desmoid tumors are considered benign (noncancerous) because they don’t spread to other areas of your body. However, sometimes desmoid tumors grow aggressively, affecting nearby structures. In very rare instances, they can be fatal.

Are desmoid tumors sarcomas?

Desmoid tumors are a type of soft-tissue tumor that come from fibrous tissue. They are related to connective tissue cancers called sarcomas, but desmoid tumors are not cancers because they do not spread to other parts of the body.

How do you shrink a desmoid tumor?

Anti-inflammatory drugs may cause the tumor to slowly shrink. Non-steroidal anti-inflammatory drugs (NSAIDs) and drugs such as Imatinib are used to treat desmoid tumors.

Are desmoid tumors malignant?

Overview. Desmoid tumors are noncancerous growths that occur in the connective tissue. Desmoid tumors most often occur in the abdomen, arms and legs. Another term for desmoid tumors is aggressive fibromatosis.

Can desmoid tumor become malignant?

Desmoid tumors aren’t considered cancers because they don’t spread to other areas of the body. But they can be very aggressive, acting more like cancers and growing into nearby structures and organs.

Is fibromatosis curable?

There is no cure for desmoid tumors; when possible, patients are encouraged to enlist in clinical trials. A biopsy is always indicated as the definitive method to determine nature of the tumour. Management of these lesions is complex, the main problem being the high rates of recurrence in FAP associated disease.

How fast do desmoid tumors grow?

[11] reported that sporadic postoperative intra-abdominal desmoid tumors can develop 11 months to 7 years after abdominal surgery. In our patient, the desmoid tumor was detected 6 months postoperatively and the new masses were detected 9 months postoperatively.